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CCDC103 Antibody

  • 中文名稱:
    CCDC103兔多克隆抗體
  • 貨號:
    CSB-PA812877LA01HU
  • 規格:
    ¥440
  • 圖片:
    • Western Blot
      Positive WB detected in: Mouse heart whole cell lysate
      All lanes:CCDC103 Antibody at 1:1000
      Secondary
      Goat polyclonal to rabbit IgG at 1/50000 dilution
      Predicted band size: 28kDa
      Observed band size: 28 kDa
  • 其他:

產品詳情

  • 產品名稱:
    Rabbit anti-Homo sapiens (Human) CCDC103 Polyclonal antibody
  • Uniprot No.:
  • 基因名:
    CCDC103
  • 別名:
    CCDC103Coiled-coil domain-containing protein 103 antibody
  • 宿主:
    Rabbit
  • 反應種屬:
    Human, Mouse
  • 免疫原:
    Recombinant Human Coiled-coil domain-containing protein 103 protein (1-242AA)
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標記方式:
    Non-conjugated

    本頁面中的產品,CCDC103 Antibody (CSB-PA812877LA01HU),的標記方式是Non-conjugated。對于CCDC103 Antibody,我們還提供其他標記。見下表:

    可提供標記
    標記方式 貨號 產品名稱 應用
    HRP CSB-PA812877LB01HU CCDC103 Antibody, HRP conjugated ELISA
    FITC CSB-PA812877LC01HU CCDC103 Antibody, FITC conjugated
    Biotin CSB-PA812877LD01HU CCDC103 Antibody, Biotin conjugated ELISA
  • 克隆類型:
    Polyclonal
  • 抗體亞型:
    IgG
  • 純化方式:
    >95%, Protein G purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, PH 7.4
  • 產品提供形式:
    Liquid
  • 應用范圍:
    ELISA, WB
  • 推薦稀釋比:
    Application Recommended Dilution
    WB 1:1000-1:5000
  • Protocols:
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能:
    Dynein-attachment factor required for cilia motility.
  • 基因功能參考文獻:
    1. The CCDC103 p.His154Pro mutation is more prevalent than previously thought in the South Asian community in the UK and causes primary ciliary dyskinesia that can be difficult to diagnose using pathology-based clinical tests. PMID: 28790179
    2. A variable and complex phenotype caused by the co-inheritance of a single gene mutation in CCDC103 and a microduplication at 17q12, both on chromosome 17. PMID: 26123568
    3. These results identify Ccdc103 as a dynein arm attachment factor that causes primary ciliary dyskinesia when mutated. PMID: 22581229
  • 相關疾病:
    Ciliary dyskinesia, primary, 17 (CILD17)
  • 亞細胞定位:
    Cytoplasm. Cell projection, cilium, flagellum.
  • 蛋白家族:
    CCDC103/PR46b family
  • 數據庫鏈接:

    HGNC: 32700

    OMIM: 614677

    KEGG: hsa:388389

    STRING: 9606.ENSP00000387252

    UniGene: Hs.743398