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GBA1

GBA1,即溶酶體酸性β-葡糖腦苷脂酶,是一種在人體細胞中廣泛分布的酶,尤其在神經元和巨噬細胞中表達豐富。其結構包含多個功能域,共同協作催化葡糖腦苷脂的水解,從而維持細胞內外葡萄糖和腦苷脂的平衡。GBA1不僅參與脂質代謝,對細胞膜的結構和功能以及細胞內的信號傳導起到關鍵作用,還與神經系統的正常功能緊密相連。其功能的異常可能導致神經退行性疾病如高雪氏癥等的發生。此外,GBA1與磷脂酰肌醇-3-激酶信號通路、自噬過程和炎癥反應等細胞內的多個信號通路密切相關,共同調控細胞的生長、增殖、凋亡以及免疫應答等生理過程。

熱銷產品

Recombinant Human Lysosomal acid glucosylceramidase (GBA1)

驗證數據

SDS
CSB-EP009289HU SDS

(Tris-Glycine gel) Discontinuous SDS-PAGE (reduced) with 5% enrichment gel and 15% separation gel.

LCMS
CSB-EP009289HU LCMS-1

Based on the SEQUEST from database of E.coli host and target protein, the LC-MS/MS Analysis result of CSB-EP009289HU could indicate that this peptide derived from E.coli-expressed Homo sapiens (Human) GBA.

LCMS
CSB-EP009289HU LCMS-2

Based on the SEQUEST from database of E.coli host and target protein, the LC-MS/MS Analysis result of CSB-EP009289HU could indicate that this peptide derived from E.coli-expressed Homo sapiens (Human) GBA.


GBA1 Antibodies

GBA1 for Homo sapiens (Human)

GBA1 Proteins

GBA1 Proteins for Homo sapiens (Human)

GBA1 ELISA Kit

GBA1 ELISA Kit for Homo sapiens (Human)